Authors :
Triani Dhamayanti; Yulius Patimang; Andi Alief Utama Armin; Muzakkir Amir
Volume/Issue :
Volume 9 - 2024, Issue 5 - May
Google Scholar :
https://tinyurl.com/mujbwm7d
Scribd :
https://tinyurl.com/2nvmuvy6
DOI :
https://doi.org/10.38124/ijisrt/IJISRT24MAY990
Note : A published paper may take 4-5 working days from the publication date to appear in PlumX Metrics, Semantic Scholar, and ResearchGate.
Abstract :
In the first place, the right ventricle is the
primary or only point of origin for both main arteries in
a patient with double outlet right ventricle (DORV). In
order to guarantee proper repair, a wide variety of
surgical approaches, considerations, and procedures are
required for the wide spectrum of disorders that make
up DORV. A functional classification based on
physiological characteristics is one technique to
classifying it, which might help determine the
appropriate surgical strategy. Presentation of the case:
Our case study focused on a female newborn infant who
was 2 months old when she arrived at the hospital
complaining of worsening shortness of breath and
anorexia. The patient was diagnosed with pulmonary
over-circulation, an abnormal accumulation of blood
flowing into the lungs, through the following cardiac
abnormalities: double outlet right ventricle (DORV)
with a non-committal ventricular septal defect (VSD),
no pulmonary stenosis (PS), mitral atresia, atrial septal
defect (ASD), single ventricle dominance (SVD),
anomalous pulmonary venous drainage (APVD), and
patent ductus arteriosus (PDA). After a palliative
procedure including the closure of the PDA and the
implantation of a PA band, the patient was to have a
surgical procedure known as univentricular repair.
During the surgical meeting, this course of action was
agreed upon. Conclusion: Different atrial
configurations, atrioventricular connections, ventricular
morphologies, and spatial interactions between the main
arteries may all contribute to the wide anatomical
spectrum of DORV. In order to decide between
biventricular repair and univentricular palliation,
several anatomical features must be present in the
patient. In addition, palliative treatments may be
necessary for certain patients before they may have a
permanent surgical repair.
Keywords :
Double Outlet Right Ventricle (DORV); Univentricular repair; Ventricular Septal Defect (VSD); Pulmonary over-circulation; Palliative treatment.
References :
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In the first place, the right ventricle is the
primary or only point of origin for both main arteries in
a patient with double outlet right ventricle (DORV). In
order to guarantee proper repair, a wide variety of
surgical approaches, considerations, and procedures are
required for the wide spectrum of disorders that make
up DORV. A functional classification based on
physiological characteristics is one technique to
classifying it, which might help determine the
appropriate surgical strategy. Presentation of the case:
Our case study focused on a female newborn infant who
was 2 months old when she arrived at the hospital
complaining of worsening shortness of breath and
anorexia. The patient was diagnosed with pulmonary
over-circulation, an abnormal accumulation of blood
flowing into the lungs, through the following cardiac
abnormalities: double outlet right ventricle (DORV)
with a non-committal ventricular septal defect (VSD),
no pulmonary stenosis (PS), mitral atresia, atrial septal
defect (ASD), single ventricle dominance (SVD),
anomalous pulmonary venous drainage (APVD), and
patent ductus arteriosus (PDA). After a palliative
procedure including the closure of the PDA and the
implantation of a PA band, the patient was to have a
surgical procedure known as univentricular repair.
During the surgical meeting, this course of action was
agreed upon. Conclusion: Different atrial
configurations, atrioventricular connections, ventricular
morphologies, and spatial interactions between the main
arteries may all contribute to the wide anatomical
spectrum of DORV. In order to decide between
biventricular repair and univentricular palliation,
several anatomical features must be present in the
patient. In addition, palliative treatments may be
necessary for certain patients before they may have a
permanent surgical repair.
Keywords :
Double Outlet Right Ventricle (DORV); Univentricular repair; Ventricular Septal Defect (VSD); Pulmonary over-circulation; Palliative treatment.