Adenoid cystic carcinoma is an infrequent tumor that forms less than 1% head and neck malignancy and 10 % of all salivary gland tumors and the common location is the palate. Here is a rare case report of adenoid cystic carcinoma of the palate with a poor prognosis. The late diagnosis resulted only in palliative treatment. Awareness of signs and symptoms should be elaborated to all primary physicians and among common people.

Keywords : Adenoid Cystic Carcinoma, Perineural Invasion, Palatal Swelling.